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Alagille syndrome.

Alagille syndrome (OMIM 118450) is an autosomal dominant disorder associated with abnormalities of the liver, heart, eye, skeleton, and a characteristic facial appearance. Also referred to as the Alagille-Watson syndrome, syndromic bile duct paucity, and arteriohepatic dysplasia, it is a significant...

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Detalles Bibliográficos
Autores principales: Krantz, I D, Piccoli, D A, Spinner, N B
Formato: Artigo
Lenguaje:Inglês
Publicado: 1997
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC1050871/
https://ncbi.nlm.nih.gov/pubmed/9039994
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