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Unusual inheritance of primary ciliary dyskinesia (Kartagener's syndrome).

Primary ciliary dyskinesia syndrome is characterised by chronic sinusitis, bronchiectasis, and, in 50% of cases, dextrocardia. It is generally believed to be inherited as an autosomal recessive disorder. In this report, we describe a family consisting of a mother and her five male children, the offs...

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Detalhes bibliográficos
Main Authors: Narayan, D, Krishnan, S N, Upender, M, Ravikumar, T S, Mahoney, M J, Dolan, T F, Teebi, A S, Haddad, G G
Formato: Artigo
Idioma:Inglês
Publicado em: 1994
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1049931/
https://ncbi.nlm.nih.gov/pubmed/8071978
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