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Genetic aspects of fibrodysplasia ossificans progressiva.

Complete ascertainment of fibrodysplasia ossificans progressiva in the United Kingdom was attempted and 44 patients were identified. This indicates a point prevalence of 0.61 x 10(-6). The disease is determined as an autosomal dominant trait which has complete penetrance but variable expressivity. N...

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Autors principals: Connor, J M, Evans, D A
Format: Artigo
Idioma:Inglês
Publicat: 1982
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1048816/
https://ncbi.nlm.nih.gov/pubmed/7069743
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