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Asplenia and polysplenia syndromes with abnormalities of lateralisation in a sibship.

In the family presented here the first child had asplenia syndrome with cor biloculare' transposition of the great vessels, pulmonary stenosis, and anomalous pulmonary venous drainage. Another sib had situs inversus with polysplenia syndrome, including very similar cardiovascular defects and bi...

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Autori principali: Zlotogora, J, Elian, E
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1981
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1048737/
https://ncbi.nlm.nih.gov/pubmed/7277426
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