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Non-penetrance in tuberous sclerosis.

Non-penetrance has not been reported in tuberous sclerosis when modern non-invasive investigations have been performed. We report a four generation family in which there was a subject with minimal expression and another with non-penetrance between a great grandfather and his great grandson. This sit...

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Autors principals: Webb, D W, Osborne, J P
Format: Artigo
Idioma:Inglês
Publicat: 1991
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC1016911/
https://ncbi.nlm.nih.gov/pubmed/1870099
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