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Autosomal dominant pseudoxanthoma elasticum

Two families are described, each with a unique clinical variant of pseudoxanthoma elasticum (PXE) inherited in autosomal dominant fashion. Dominant type I PXE is characterized by a classical flexurally distributed rash, severe and frequent angina of effort, intermittent claudication and hypertension...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awdur: Pope, F. M.
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: 1974
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC1013111/
https://ncbi.nlm.nih.gov/pubmed/4841083
Tagiau: Ychwanegu Tag
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