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Hemophagocytic lymphohistiocytosis presenting in a pediatric patient with near total colonic and small bowel aganglionosis: a case report

Abstract Background Total colonic and small bowel aganglionosis is a rare condition typically requiring intestinal transplant for long-term survival. There have not been any previously reported cases of near total intestinal aganglionosis complicated by concerns for hemophagocytic lymphohistiocytosi...

पूर्ण विवरण

में बचाया:
ग्रंथसूची विवरण
मुख्य लेखकों: Brittany Badal, Michael J. Wilsey, Sara Karjoo
स्वरूप: Artigo
भाषा:Inglês
प्रकाशित: BMC 2017-08-01
श्रृंखला:Journal of Medical Case Reports
विषय:
ऑनलाइन पहुंच:http://link.springer.com/article/10.1186/s13256-017-1390-4
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