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Successful whole lung lavage in pulmonary alveolar proteinosis secondary to lysinuric protein intolerance: a case report

<p>Abstract</p> <p>Background</p> <p>Pulmonary alveolar proteinosis (PAP) is a rare disease characterised by accumulation of lipoproteinaceous material within alveoli, occurring in three clinically distinct forms: congenital, acquired and secondary. Among the latter, ly...

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Библиографические подробности
Главные авторы: Baritussio Aldo, Bolongaro Antonia, Adami Andrea, Stella Giulia M, Rodi Giuseppe, Ceruti Michele, Pozzi Ernesto, Luisetti Maurizio
Формат: Artigo
Язык:Inglês
Опубликовано: BMC 2007-03-01
Серии:Orphanet Journal of Rare Diseases
Online-ссылка:http://www.OJRD.com/content/2/1/14
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