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Prevalence and clinical outcomes of fibrotic interstitial lung disease in ANCA associated vasculitis: a single-centre, retrospective, cohort study

Abstract Background Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) may affect multiple organs and interstitial lung disease (ILD) might be the first manifestation. Limited and discordant data are available on the prevalence of ILD in patients with AAV. Little is known about p...

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Autors principals: Claudio Tirelli, Sabrina Mira, Tommaso Schioppo, Sara Mirijaj, Marta Italia, Francesca Pescol, Simone Frizzarin, Cristina Albrici, Fausta Alfano, Lucia Sacchi, Gian Marco Podda, Mario Gennaro Cozzolino, Michele Mondoni
Format: Artigo
Idioma:Inglês
Publicat: BMC 2026-02-01
Col·lecció:Respiratory Research
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Accés en línia:https://doi.org/10.1186/s12931-026-03570-0
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