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Reversal of hemochromatosis by apotransferrin in non-transfused and transfused Hbbth3/+ (heterozygous b1/b2 globin gene deletion) mice

Intermediate beta-thalassemia has a broad spectrum of sequelae and affected subjects may require occasional blood transfusions over their lifetime to correct anemia. Iron overload in intermediate beta-thalassemia results from a paradoxical intestinal absorption, iron release from macrophages and hep...

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Autori principali: Monique P. Gelderman, Jin Hyen Baek, Ayla Yalamanoglu, Michele Puglia, Florence Vallelian, Bo Burla, Jaroslav Vostal, Dominik J. Schaer, Paul W. Buehler
Natura: Artigo
Lingua:Inglês
Pubblicazione: Ferrata Storti Foundation 2015-05-01
Serie:Haematologica
Accesso online:https://haematologica.org/article/view/7369
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