Segmental Absence of Intestinal Musculature in a Child with Type IV Ehlers–Danlos Syndrome

Patients with vascular Ehlers–Danlos syndrome (vEDS) have a defect in the formation of type III collagen. This defect puts patients at risk of vascular rupture, uterine rupture, and bowel perforations. The segmental absence of intestinal musculature is a rare histopathologic finding, wherein there i...

ver descrição completa

Detalhes bibliográficos

Principais autores:	Nicole Zeky, Celia Short, Brent Keith, Randall D. Craver, Jessica A. Zagory
Formato:	Artigo
Idioma:	Inglês
Publicado em:	MDPI AG 2021-08-01
coleção:	Children
Assuntos:	Ehlers–Danlos vascular Ehlers–Danlos intestinal perforation segmental absence of intestinal musculature
Acesso em linha:	https://www.mdpi.com/2227-9067/8/8/680
Tags:	Adicionar Tag Sem tags, seja o primeiro a adicionar uma tag!