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Case Report: Malignant perivascular epithelioid cell tumor with aggressive mediastinal invasion and pulmonary metastasis

Perivascular epithelioid cell tumors (PEComas) are rare, typically benign soft tissue tumors that can develop at various anatomic sites. Malignant PEComas are rarer entities but may present aggressively with metastasis to the lungs or local recurrence years after initial presentation. In unresectabl...

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Main Authors: Daniel F. Leach, Srivikram Margam S, Marissa Foster, Jarrod B. Adkison
Formato: Artigo
Idioma:Inglês
Publicado: Frontiers Media S.A. 2025-08-01
Series:Frontiers in Oncology
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Acceso en liña:https://www.frontiersin.org/articles/10.3389/fonc.2025.1551663/full
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