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Clinical features, treatment strategies, and long-term outcomes of Blau syndrome: a 10-year experience from a Chinese cohort

Abstract Objectives Blau syndrome (BS) is a rare autoinflammatory disorder characterized by the clinical triad of uveitis, dermatitis, and arthritis. While the clinical spectrum is well-documented, data on the longitudinal efficacy and durability of tumor necrosis factor-α (TNF-α) inhibitors remain...

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Autores principales: Jingyuan Zhang, Min Shen
Formato: Artigo
Lenguaje:Inglês
Publicado: BMC 2026-02-01
Colección:Advances in Rheumatology
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Acceso en línea:https://doi.org/10.1186/s42358-026-00528-0
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