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The Effect of Adiposity on Cardiovascular Function and Myocardial Fibrosis in Patients With Duchenne Muscular Dystrophy

Background Patients with Duchenne muscular dystrophy (DMD) develop cardiomyopathy because of a dystrophin deficiency causing fibrofatty replacement of the myocardium. Corticosteroid use and mobility limitations place these patients at risk for increased adiposity. We sought to determine the associat...

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Auteurs principaux: Sarah E. Henson, Sean M. Lang, Philip R. Khoury, Cuixia Tian, Meilan M. Rutter, Elaine M. Urbina, Thomas D. Ryan, Michael D. Taylor, Tarek Alsaied
Format: Artigo
Langue:Inglês
Publié: Wiley 2021-10-01
Collection:Journal of the American Heart Association: Cardiovascular and Cerebrovascular Disease
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Accès en ligne:https://www.ahajournals.org/doi/10.1161/JAHA.121.021037
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