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P130 | LIVER TRANSPLANT IN CONGENITAL AFIBRINOGENEMIA: A CASE REPORT

Background: Fibrinogen (FBG) is involved in the final steps of coagulation as a precursor of fibrin monomers. Inherited FBG disorders are generally classified as quantitative or qualitative. Quantitative disorders include afibrinogenemia (aFBG), which is characterized by the complete absence of FBG....

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Autors principals: G. Murante, S. Bergonzi, C. Sella, F. Valeri, C. Dainese, A. Valpreda, R. Pastorino, R. Romagnoli, D. Patrono, D. Cussa, S. Martini, B. Bruno, and A. Borchiellini
Format: Artigo
Idioma:Inglês
Publicat: Ferrata Storti Foundation 2025-09-01
Col·lecció:Haematologica
Accés en línia:https://haematologica.org/article/view/12427
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