Fatal rupture of pulmonary arteriovenous malformation in hereditary haemorrhagic telangiectasis and severe PAH

29-yr-old patient with hereditary haemorrhagic telangiectasia was referred to the present authors’ centre with progressive exertional dyspnoea. Pulmonary arterial hypertension (PAH) was suspected on Doppler echocardiography and confirmed by right heart catheterisation demonstrating severe PAH. Genet...

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Detalhes bibliográficos

Principais autores:	D. Montani, L. C. Price, B. Girerd, T. Chinet, P. Lacombe, G. Simonneau, M. Humbert
Formato:	Artigo
Idioma:	Inglês
Publicado em:	European Respiratory Society 2009-03-01
coleção:	European Respiratory Review
Assuntos:	Activin receptor-like kinase-1 arteriovenous malformation embolisation hereditary haemorrhagic telangiectasia pulmonary arterial hypertension rupture
Acesso em linha:	http://err.ersjournals.com/cgi/content/full/18/111/42
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