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A Case of Von Hippel-Lindau Disease Presented with Multiple Pancreatic Cysts and Medullary Hemangioblastoma

Von Hippel-Lindau (VHL) disease is a rare inherited cancer predisposition syndrome characterized by benign and malignant tumors in multiple organs, especially cerebellar hemangioblastomas, retinal angiomas, renal-cell carcinoma, and pheochromocytomas. Clinically, VHL disease also presents an increas...

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Autori principali: Young Hyun Kim, Hye Lim Jung, Aram Yang, Ji Hee Kwak, Deok Soo Kim, Jung Yeon Shim, Jae Won Shim
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Korean Society of Pediatric Hematology-Oncology 2020-04-01
Serie:Clinical Pediatric Hematology-Oncology
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Accesso online:https://doi.org/10.15264/cpho.2020.27.1.67
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