Anaesthetic considerations for liver transplantation in propionic acidemia

Propionic acidemia (PA) is an autosomal recessive disorder of metabolism due to deficiency of the enzyme propionyl-CoA carboxylase (PCC) that converts propionyl-CoA to methylmalonyl-CoA with the help of the cofactor biotin inside the mitochondria. The resultant accumulation of propionyl-CoA causes s...

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Autores principales:	Akila Rajakumar, Ilankumaran Kaliamoorthy, Mettu Srinivas Reddy, Mohamed Rela
Formato:	Artigo
Lenguaje:	Inglês
Publicado:	Wolters Kluwer Medknow Publications 2016-01-01
Colección:	Indian Journal of Anaesthesia
Materias:	Hyperammonaemic crisis, inborn metabolic errors, liver transplantation, organic acidemia, propionic acidemia and anaesthesia
Acceso en línea:	http://www.ijaweb.org/article.asp?issn=0019-5049;year=2016;volume=60;issue=1;spage=50;epage=54;aulast=Rajakumar
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