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Liver transplantation in glycogen storage disease type Ib: The role of SGLT2 inhibitors

We report on liver transplantation in two patients with GSD Ib on treatment with empagliflozin. The use of this SGLT2 inhibitor resulted in a marked decrease of 1,5-anhydroglucitol which has an important role in the development of neutropenia in this condition. As intended, this caused a significant...

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Principais autores: Simona Murko, Manuela Peschka, Konstantinos Tsiakas, Sebastian Schulz-Jürgensen, Uta Herden, René Santer
Formato: Artigo
Idioma:Inglês
Publicado: Elsevier 2023-06-01
Series:Molecular Genetics and Metabolism Reports
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Acceso en liña:http://www.sciencedirect.com/science/article/pii/S221442692300023X
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