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Neutrophil serine proteases in cystic fibrosis: role in disease pathogenesis and rationale as a therapeutic target

Chronic airway inflammation is a central feature in the pathogenesis of bronchiectasis (BE), which can be caused by cystic fibrosis (CFBE; hereafter referred to as CF lung disease) and non-CF-related conditions (NCFBE). Inflammation in both CF lung disease and NCFBE is predominantly driven by neutro...

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Principais autores: Marcus A. Mall, Jane C. Davies, Scott H. Donaldson, Raksha Jain, James D. Chalmers, Michal Shteinberg
Formato: Artigo
Idioma:Inglês
Publicado: European Respiratory Society 2024-09-01
Series:European Respiratory Review
Acceso en liña:http://err.ersjournals.com/content/33/173/240001.full
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