Case Report: Treatment of porphyria cutanea tarda with low dose hydroxychloroquine [version 1; peer review: 1 approved, 2 approved with reservations]
Background: Porphyria cutanea tarda (PCT) is a complex metabolic disease resulting from altered activity of the enzyme uroporphyrinogen decarboxylase (UROD) in the liver resulting in accumulation of uroporphyrin. PCT presents as a blistering photodermatitis with skin fragility, vesicles, scarring an...
-д хадгалсан:
| Үндсэн зохиолчид: | , , |
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| Формат: | Artigo |
| Хэл сонгох: | Inglês |
| Хэвлэсэн: |
F1000 Research Ltd
2022-08-01
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| Цуврал: | F1000Research |
| Нөхцлүүд: | |
| Онлайн хандалт: | https://f1000research.com/articles/11-945/v1 |
| Шошгууд: |
Шошго байхгүй, Энэхүү баримтыг шошголох эхний хүн болох!
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