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Case Report: Treatment of porphyria cutanea tarda with low dose hydroxychloroquine [version 1; peer review: 1 approved, 2 approved with reservations]

Background: Porphyria cutanea tarda (PCT) is a complex metabolic disease resulting from altered activity of the enzyme uroporphyrinogen decarboxylase (UROD) in the liver resulting in accumulation of uroporphyrin. PCT presents as a blistering photodermatitis with skin fragility, vesicles, scarring an...

Бүрэн тодорхойлолт

-д хадгалсан:
Номзүйн дэлгэрэнгүй
Үндсэн зохиолчид: Alexander Nirenberg, Andrew Awad, Rodney Sinclair
Формат: Artigo
Хэл сонгох:Inglês
Хэвлэсэн: F1000 Research Ltd 2022-08-01
Цуврал:F1000Research
Нөхцлүүд:
Онлайн хандалт:https://f1000research.com/articles/11-945/v1
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