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Activin signaling inhibitor Sotatercept in pulmonary veno-occlusive disease: building a bridge to transplantation?

Background: Pulmonary veno-occlusive disease (PVOD) is a rare form of pulmonary arterial hypertension (PAH). Its prognosis is considerably worse and no medical treatment has a proven efficacy. Vasodilating drugs for PAH may contribute to a pulmonary edema in PVOD. Sotatercept is the latest approved...

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Bibliografiske detaljer
Principais autores: Marcel Mietzner, Matthias Held, Elena Pfeuffer-Jovic
Format: Artigo
Sprog:Inglês
Udgivet: Elsevier 2026-01-01
Serier:Respiratory Medicine Case Reports
Fag:
Online adgang:http://www.sciencedirect.com/science/article/pii/S2213007126000857
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