Activin signaling inhibitor Sotatercept in pulmonary veno-occlusive disease: building a bridge to transplantation?
Background: Pulmonary veno-occlusive disease (PVOD) is a rare form of pulmonary arterial hypertension (PAH). Its prognosis is considerably worse and no medical treatment has a proven efficacy. Vasodilating drugs for PAH may contribute to a pulmonary edema in PVOD. Sotatercept is the latest approved...
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| Principais autores: | , , |
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| Format: | Artigo |
| Sprog: | Inglês |
| Udgivet: |
Elsevier
2026-01-01
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| Serier: | Respiratory Medicine Case Reports |
| Fag: | |
| Online adgang: | http://www.sciencedirect.com/science/article/pii/S2213007126000857 |
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