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Primary pulmonary lymphangiectasia in Noonan syndrome: apropos of an extremely rare manifestation and a brief literature review

Noonan syndrome (NS) is a genetic multisystem disorder characterised by distinctive facial features, developmental delay, learning difficulties, short stature, congenital heart disease, renal anomalies, bleeding difficulties and lymphatic malformations. Although lymphatic dysplasias are present in 2...

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Detalhes bibliográficos
Principais autores: Georgia-Emmanuela Dendrinou, Panagiotis Zagarelos, Angelos Sofronas, Stamatis Katsenos
Formato: Artigo
Idioma:Inglês
Publicado em: PAGEPress Publications 2020-12-01
coleção:Monaldi Archives for Chest Disease
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Acesso em linha:https://monaldi-archives.org/index.php/macd/article/view/1576
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