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Molecular Mechanisms of Aggregation of Canine SOD1 E40K Amyloidogenic Mutant Protein

Canine degenerative myelopathy (DM) is a human amyotrophic lateral sclerosis (ALS)-like neurodegenerative disease. It is a unique, naturally occurring animal model of human ALS. Canine DM is associated with the aggregation of canine superoxide dismutase 1 (cSOD1), which is similar to human ALS. Almo...

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Principais autores: Kento Wakayama, Shintaro Kimura, Yui Kobatake, Hiroaki Kamishina, Naohito Nishii, Satoshi Takashima, Ryo Honda, Yuji O. Kamatari
Formato: Artigo
Idioma:Inglês
Publicado: MDPI AG 2022-12-01
Series:Molecules
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Acceso en liña:https://www.mdpi.com/1420-3049/28/1/156
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