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The Role of Iron in Friedreich’s Ataxia: Insights From Studies in Human Tissues and Cellular and Animal Models

Friedreich’s ataxia (FRDA) is a rare early-onset degenerative disease that affects both the central and peripheral nervous systems, and other extraneural tissues, mainly the heart and endocrine pancreas. This disorder progresses as a mixed sensory and cerebellar ataxia, primarily disturbing the prop...

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Autori principali: José Vicente Llorens, Sirena Soriano, Pablo Calap-Quintana, Pilar Gonzalez-Cabo, María Dolores Moltó
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2019-02-01
Serie:Frontiers in Neuroscience
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Accesso online:https://www.frontiersin.org/article/10.3389/fnins.2019.00075/full
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