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Deciphering the clinical profile and diagnostic framework of hemophagocytic lymphohistiocytosis in a tertiary care setting

Background: Hemophagocytic lymphohistiocytosis (HLH) is a severe hyperinflammatory disorder marked by intense yet ineffective immune activation, resulting in hemophagocytosis, systemic inflammation, and multi-organ dysfunction. The diagnosis has traditionally depended on the 2004 HLH criteria, while...

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Principais autores: Lipsa Priyadarshini, Meenakshi Mohapatro, Priyadarshini Biswal, Silla Alisha Patro, Devidutta Ramani Ranjan Rout, Simadri Swetapadma Roul
Formato: Artigo
Idioma:Inglês
Publicado em: Wolters Kluwer Medknow Publications 2024-12-01
coleção:MGM Journal of Medical Sciences
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Acesso em linha:https://doi.org/10.4103/mgmj.mgmj_321_24
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