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Non-Enzymatic Formation of <i>N</i>-acetylated Amino Acid Conjugates in Urine

Unknown <i>N</i>-acylated amino acid (<i>N</i>-AAA) conjugates have been detected in maple syrup urine disease (MSUD) and other inborn errors of metabolism (IEMs). This study aimed to elucidate the mechanism behind the formation of urinary <i>N</i>-AAA conjugates. Liquid–liquid extraction was employ...

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Detaylı Bibliyografya
Asıl Yazarlar: Jano Jacobs, Cornelia Gertina Catharina Elizabeth van Sittert, Lodewyk Japie Mienie, Marli Dercksen, Monique Opperman, Barend Christiaan Vorster
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: MDPI AG 2023-09-01
Seri Bilgileri:Applied Sciences
Konular:
Online Erişim:https://www.mdpi.com/2076-3417/13/18/10002
Etiketler: Etiketle
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