CoQ deficiency causes disruption of mitochondrial sulfide oxidation, a new pathomechanism associated with this syndrome

Abstract Coenzyme Q (CoQ) is a key component of the mitochondrial respiratory chain, but it also has several other functions in the cellular metabolism. One of them is to function as an electron carrier in the reaction catalyzed by sulfide:quinone oxidoreductase (SQR), which catalyzes the first reac...

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Detalhes bibliográficos

Principais autores:	Marta Luna‐Sánchez, Agustín Hidalgo‐Gutiérrez, Tatjana M Hildebrandt, Julio Chaves‐Serrano, Eliana Barriocanal‐Casado, Ángela Santos‐Fandila, Miguel Romero, Ramy KA Sayed, Juan Duarte, Holger Prokisch, Markus Schuelke, Felix Distelmaier, Germaine Escames, Darío Acuña‐Castroviejo, Luis C López
Formato:	Artigo
Idioma:	Inglês
Publicado em:	Springer Nature 2016-11-01
coleção:	EMBO Molecular Medicine
Assuntos:	blood pressure COX glutathione mitochondrial disease SQR
Acesso em linha:	https://doi.org/10.15252/emmm.201606345
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