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Cardiac device implantation and device usage in Fabry and hypertrophic cardiomyopathy

Abstract Background Fabry disease (FD) is a treatable X-linked condition leading to progressive cardiac disease, arrhythmia and premature death. We aimed to increase awareness of the arrhythmogenicity of Fabry cardiomyopathy, by comparing device usage in patients with Fabry cardiomyopathy and sarcom...

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Autors principals: Ravi Vijapurapu, William Bradlow, Francisco Leyva, James C. Moon, Abbasin Zegard, Nigel Lewis, D. Kotecha, Ana Jovanovic, Derralynn A. Hughes, Peter Woolfson, Richard P. Steeds, Tarekegn Geberhiwot
Format: Artigo
Idioma:Inglês
Publicat: BMC 2022-01-01
Col·lecció:Orphanet Journal of Rare Diseases
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Accés en línia:https://doi.org/10.1186/s13023-021-02133-4
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