Synchrotron‐Based Phase‐Contrast Micro‐CT Combined With Histology to Decipher Differences Between Hereditary and Sporadic Pediatric Pulmonary Veno‐Occlusive Disease

ABSTRACT Pulmonary veno‐occlusive disease (PVOD) is a lethal variant of pulmonary hypertension. The degree of pulmonary arterial involvement varies. Here, we compare two PVOD patients who were transplanted at 8 years of age, whereof one is a homozygous EIF2AK4 mutation carrier. Tissue was imaged wit...

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Autori principali:	Ida Jeremiasen, Niccolò Peruzzi, Elna Lampei, Sofie Meyer, Levent M. Akyürek, Erik Gebre‐Medhin, Ceren Mutgan, Peter Dorfmüller, Lavinia Neubert, Danny Jonigk, Csaba Galambos, Karin Tran‐Lundmark
Natura:	Artigo
Lingua:	Inglês
Pubblicazione:	Wiley 2024-10-01
Serie:	Pulmonary Circulation
Soggetti:	children EIF2AK4 mutation pulmonary hypertension pulmonary veno‐occlusive disease synchrotron
Accesso online:	https://doi.org/10.1002/pul2.70024
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