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The importance of terminal complement inhibition in paroxysmal nocturnal hemoglobinuria

Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, chronic hematologic disorder associated with inappropriate terminal complement activity on blood cells that can result in intravascular hemolysis (IVH), thromboembolic events (TEs), and organ damage. Untreated individuals with PNH have an increase...

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Autors principals: Austin G. Kulasekararaj, Robert A. Brodsky, Jun-ichi Nishimura, Christopher J. Patriquin, Hubert Schrezenmeier
Format: Artigo
Idioma:Inglês
Publicat: SAGE Publishing 2022-05-01
Col·lecció:Therapeutic Advances in Hematology
Accés en línia:https://doi.org/10.1177/20406207221091046
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