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Immunohistochemical alterations of dystrophin in congenital muscular dystrophy Alterações imuno-hístoquímicas da distrofina na distrofia muscular congênita

The dystrophin distribution in the plasma muscle membrane using immunohystochemistry was studied in 22 children with congenital muscular dystrophy. The dystrophin was detected by immunofluorescence in muscle biopsy through a polyclonal antibody. All the cases had patchy interruptions of the fluoresc...

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Détails bibliographiques
Auteurs principaux: Lineu Cesar Werneck, Eduardo Bonilla
Format: Artigo
Langue:Inglês
Publié: Thieme Revinter Publicações 1995-09-01
Collection:Arquivos de Neuro-Psiquiatria
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Accès en ligne:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1995000300008
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