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Blau syndrome complicated by granulomatous tubulointerstitial nephritis and immune complex mediated glomerulonephritis: A case report and review of the literature

Blau syndrome is a rare, autosomal dominant or de novo mutation, granulomatous, auto-inflammatory disorder classically manifesting as a triad of polyarthritis, uveitis, and dermatitis. Rarely, this disease involves visceral sites such as the liver, lung, and kidney. In this report, we describe a cas...

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Autors principals: Kelly M. Garrity, Richard Chiu, Rachana Srivastava, Deborah K. McCurdy, Jonathan E. Zuckerman
Format: Artigo
Idioma:Inglês
Publicat: Elsevier 2024-03-01
Col·lecció:Human Pathology Reports
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Accés en línia:http://www.sciencedirect.com/science/article/pii/S2772736X24000021
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