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Pediatric CNS-isolated hemophagocytic lymphohistiocytosis with brain hemorrhages: a case report

Abstract Background Hemophagocytic lymphohistiocytosis (HLH) is an inherited syndrome characterized by immune dysregulation. Central nervous system (CNS)-isolated disease is a rare presentation of familial HLH. We present a case of pediatric CNS-isolated HLH with a presentation complicated by unusua...

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Autori principali: Mauricio Borda, Helen Tian, Steven Benitez, Ashley Bonheur, Nagma Dalvi, Ellen Fraint
Natura: Artigo
Lingua:Inglês
Pubblicazione: BMC 2024-10-01
Serie:BMC Neurology
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Accesso online:https://doi.org/10.1186/s12883-024-03840-8
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