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Severe pulmonary alveolar proteinosis with respiratory failure treated by intrapulmonary percussive ventilation

Abstract Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by abnormal accumulation of surfactant in the alveoli. Whole lung lavage (WLL) is the standard treatment for severe autoimmune PAP (aPAP); however, it is highly invasive. Intrapulmonary percussive ventilation (IPV) is a no...

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Autori principali: Takahiro Tashiro, Yusuke Tomita, Megumi Inaba, Kumiko Hayashi, Naomi Hirata, Takuro Sakagami
Natura: Artigo
Lingua:Inglês
Pubblicazione: Wiley 2020-12-01
Serie:Respirology Case Reports
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Accesso online:https://doi.org/10.1002/rcr2.676
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