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Pediatric antineutrophil cytoplasmic antibody-associated vasculitis: A review on pulmonary manifestations, management, and outcomes

Antineutrophil cytoplasm antibody (ANCA)-associated vasculitis (AAV) is a rare systemic autoimmune disorder characterized by necrotizing inflammation of blood vessels infiltrated by neutrophils. It includes three distinct entities: granulomatosis with polyangiitis (GPA, formerly known as Wegener’s g...

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Hlavní autoři: Chien-Heng Lin, Chieh-Ho Chen, Wei-Ching Lin, Wen-Jue Soong, Syuan-Yu Hong
Médium: Artigo
Jazyk:Inglês
Vydáno: Wolters Kluwer Medknow Publications 2024-09-01
Edice:Tungs’ Medical Journal
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On-line přístup:https://journals.lww.com/tmj/fulltext/2024/09001/pediatric_antineutrophil_cytoplasmic.3.aspx
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