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Heart failure in Fabry disease revisited: application of current heart failure guidelines and recommendations

Abstract Aims Fabry disease (FD) is often associated with heart failure (HF). However, data on HF prevalence, prognosis, and applicability of echocardiographic criteria for HF diagnosis in FD remain uncertain. Methods and results We evaluated patients with genetically proven FD for symptoms and natr...

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Autors principals: Daniel Rob, Josef Marek, Gabriela Dostalova, Ales Linhart
Format: Artigo
Idioma:Inglês
Publicat: Oxford University Press 2022-12-01
Col·lecció:ESC Heart Failure
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Accés en línia:https://doi.org/10.1002/ehf2.14091
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