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Effectiveness of caplacizumab in the first-line treatment for acquired thrombotic thrombocytopenic purpura: single center experience

Acquired thrombotic thrombocytopenic purpura (aTTP) is a very rare life-threatening disorder, which manifests as a profound thrombocytopenia, microangiopathic hemolytic anemia, renal insufficiency, neurological dysfunction, and other ischemic organ damage. It is caused by antibodies blocking ADAMTS1...

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Detalhes bibliográficos
Principais autores: Kristina Maria Belakova, Renata Pizurova, Tomas Simurda, Ivana Plamenova, Pavol Holly, Ingrid Skornova, Sohaib Mukhtar Agouba, Miroslava Drotarova, Monika Brunclikova, Alena Stryckova, Richard Jusko, Jan Stasko, Juraj Sokol, Alena Jezikova
Formato: Artigo
Idioma:Inglês
Publicado em: SAGE Publishing 2026-02-01
coleção:Therapeutic Advances in Hematology
Acesso em linha:https://doi.org/10.1177/20406207261419903
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