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Tracking muscle wasting and disease activity in facioscapulohumeral muscular dystrophy by qualitative longitudinal imaging

Abstract Background Facioscapulohumeral muscular dystrophy (FSHD) is one of the most frequent late‐onset muscular dystrophies, characterized by progressive fatty replacement and degeneration involving single muscles in an asynchronous manner. With clinical trials at the horizon in this disease, the...

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Principais autores: Mauro Monforte, Francesco Laschena, Pierfrancesco Ottaviani, Maria Rosaria Bagnato, Anna Pichiecchio, Giorgio Tasca, Enzo Ricci
格式: Artigo
語言:Inglês
出版: Wiley 2019-12-01
叢編:Journal of Cachexia, Sarcopenia and Muscle
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在線閱讀:https://doi.org/10.1002/jcsm.12473
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