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Plasma lipidomic analysis shows a disease progression signature in mdx mice

Abstract Duchenne muscular dystrophy (DMD) is a rare genetic disorder affecting paediatric patients. The disease course is characterized by loss of muscle mass, which is rapidly substituted by fibrotic and adipose tissue. Clinical and preclinical models have clarified the processes leading to muscle...

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Bibliografiske detaljer
Principais autores: Roula Tsonaka, Alexandre Seyer, Annemieke Aartsma-Rus, Pietro Spitali
Format: Artigo
Sprog:Inglês
Udgivet: Nature Portfolio 2021-06-01
Serier:Scientific Reports
Online adgang:https://doi.org/10.1038/s41598-021-92406-6
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