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Comparative Analysis of Perivascular Adipose Tissue Attenuation on Chest Computed Tomography Angiography in Patients with Marfan Syndrome: A Case–Control Study

<b>Background</b>: Marfan syndrome (MFS) is a rare autosomal dominant disorder affecting connective tissues due to mutations in the fibrillin-1 gene. These genetic changes often result in severe cardiovascular conditions, including asymptomatic thoracic aortic dilation potentially leading to dissect...

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Principais autores: Domenico Tuttolomondo, Francesco Secchi, Nicola Gaibazzi, Nathasha Samali Udugampolage, Alessandro Pini, Massimo De Filippo, Pietro Spagnolo, Rosario Caruso, Jacopo Taurino
Formato: Artigo
Idioma:Inglês
Publicado: MDPI AG 2025-03-01
Series:Diagnostics
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Acceso en liña:https://www.mdpi.com/2075-4418/15/6/673
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