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Management of congenital dysfibrinogenemia in pregnancy: A challenging patient case

Abstract Afibrinogenemia and congenital dysfibrinogenemia (CD) are rare conditions with limited information available for appropriate management. Previous case reports have demonstrated the safe and efficacious use of fibrinogen replacement therapy (FRT) as a therapeutic approach to prevent hemorrha...

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Autors principals: Megan Langer, Meredith Manire, Matthew Clarkson, Yazan Samhouri, Deep Shah, Rama Bhagavatula
Format: Artigo
Idioma:Inglês
Publicat: Elsevier 2021-12-01
Col·lecció:Research and Practice in Thrombosis and Haemostasis
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Accés en línia:https://doi.org/10.1002/rth2.12619
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