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When and how ruling out cystic fibrosis in adult patients with bronchiectasis

Abstract Background Bronchiectasis is the final result of different processes and most of the guidelines advocate for a careful evaluation of those etiologies which might be treated or might change patients’ management, including cystic fibrosis (CF). Main body CFTR mutations have been reported with...

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書誌詳細
主要な著者: Andrea Gramegna, Stefano Aliberti, Manuela Seia, Luigi Porcaro, Vera Bianchi, Carlo Castellani, Paola Melotti, Claudio Sorio, Enza Consalvo, Elisa Franceschi, Francesco Amati, Martina Contarini, Michele Gaffuri, Luca Roncoroni, Barbara Vigone, Angela Bellofiore, Cesare Del Monaco, Martina Oriano, Leonardo Terranova, Maria Francesca Patria, Paola Marchisio, Baroukh M. Assael, Francesco Blasi
フォーマット: Artigo
言語:Inglês
出版事項: Mattioli 1885 2018-08-01
シリーズ:Multidisciplinary Respiratory Medicine
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オンライン・アクセス:http://link.springer.com/article/10.1186/s40248-018-0142-7
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