Outcome of primary hemophagocytic lymphohistiocytosis: a report on 143 patients from the Italian Registry

Primary hemophagocytic lymphohistiocytosis (pHLH) is a severe, life-threatening hyperinflammatory syndrome caused by defects in genes of the granule-dependent cytotoxic pathway. Here we investigated the clinical presentation and outcome in a large cohort of 143 patients with pHLH diagnosed in the...

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Xehetasun bibliografikoak

Egile Nagusiak:	Francesco Pegoraro, Aurora Chinnici, Linda Beneforti, Michele Tanturli, Irene Trambusti, Carmela De Fusco, Concetta Micalizzi, Veronica Barat, Simone Cesaro, Stefania Gaspari, Fabiola Dell’Acqua, Alessandra Todesco, Fabio Timeus, Maurizio Aricò, Claudio Favre, Annalisa Tondo, Maria Luisa Coniglio, Elena Sieni, AIEOP Histiocytosis Working Group
Formatua:	Artigo
Hizkuntza:	Inglês
Argitaratua:	Ferrata Storti Foundation 2024-02-01
Saila:	Haematologica
Sarrera elektronikoa:	https://haematologica.org/article/view/11458
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