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Darier's disease with esophageal involvement, a case report.

Darier's disease (DD) is an autosomal dominant dermatosis caused by mutation of ATP2A2 gene at 12q23-24, characterized histologically by acantholysis and dyskeratosis1. It's a rare disease, distinguish by the presence of red-brown keratotic papules of follicular, palm-plantar, nail and less often in...

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Autors principals: Luzia Bismarck, Manuel Ribeiro, Marina Coelho, Fátima Monteiro, Ana Costa
Format: Artigo
Idioma:Inglês
Publicat: Sociedade Galega de Medicina Interna 2026-03-01
Col·lecció:Galicia Clínica
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Accés en línia:https://galiciaclinica.info/gc/article/view/1377
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