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Exploring glucocorticoid receptor signalling in lymphangioleiomyomatosis

Background Lymphangioleiomyomatosis (LAM) is a rare, low-grade neoplasm that causes progressive cystic lung destruction and is often associated with renal angiomyolipomas (AMLs). Given evidence of pleiotropy linking LAM risk to pulmonary traits, we investigated whether glucocorticoid receptor (GR) s...

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Principais autores: Alexandra Baiges, Lara Ruiz-Auladell, Irene García, Raúl Rigo-Bonnin, Yan Tang, Elias J. Bou-Farhat, Roderic Espín, Rosario T. Sanz, Guillermo Pablo Vicent, Mercè Donate-Castillo, Arzoo Shabbir, Jonathan Adams-Furmanski, Carmen Herranz-Ors, Rosalía Laporta, Clara Salas, Piedad Ussetti, Claudia Valenzuela, Julio Ancochea, José A. Rodríguez-Portal, María Molina-Molina, Álvaro Casanova, Eva Revilla-López, Luis Gómez-Carrera, Xavier Matias-Guiu, Miguel Angel Pavón, Dominik Jung, Hagen S. Bachmann, Ramón Manuel Lago-Lestón, Laura Muinelo-Romay, Xavier Farré, Rafael de Cid, Calvin S. Leung, Anthony S. Zannas, Manel Esteller, Jacobo Sellares, Katarzyna Błasińska, Adriana Róży, Paulina Skrońska, Antonio Gómez, Marina K. Holz, Julie S. Di Martino, David Monk, Charlotte Sefton, Leanne Walker, Anne White, Debbie Clements, Suzanne Miller, Simon R. Johnson, Hazel J. Hunt, Elizabeth P. Henske, David Kwiatkowski, Elżbieta Radzikowska, Francesca Mateo, Miquel Angel Pujana
פורמט: Artigo
שפה:Inglês
יצא לאור: European Respiratory Society 2026-06-01
סדרה:ERJ Open Research
גישה מקוונת:https://doi.org/10.1183/23120541.01285-2025
תגים: הוספת תג
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