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Changes in the cortical GABAergic inhibitory system in a Spinal Muscular Atrophy mouse model

Abstract The cortical motor network excitatory-inhibitory (E/I) imbalance contributes to several neurodegenerative movement disorders. Spinal Muscular Atrophy (SMA) is a neuromuscular disease due to the lack of Survival Motor Neuron (SMN) protein, characterized by lower motor neuron (MN) degeneratio...

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Autors principals: Giovanna Menduti, Francesco Ferrini, Anna Caretto, Amber Hassan, Raffaella di Vito, Giada Beltrando, Davide Marnetto, Alessandro Usiello, Ferdinando Di Cunto, Marina Boido, Alessandro Vercelli
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group 2026-02-01
Col·lecció:Cell Death and Disease
Accés en línia:https://doi.org/10.1038/s41419-026-08520-8
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