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Late presentation of alveolar capillary dysplasia with misalignment of pulmonary veins presenting as refractory pulmonary hypertension in infancy

Background: Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACD-MPV) is a rare congenital lung disorder characterized by abnormal pulmonary vascular and alveolar–capillary development, resulting in severe pulmonary hypertension (PH) that is typically refractory to therapy. Mos...

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Autores principales: Tamer Abusido, Saleh Alshaibi, Abdullah Aldraihem, Abdulmajeed Alfadhel
Formato: Artigo
Lenguaje:Inglês
Publicado: Elsevier 2026-01-01
Colección:Respiratory Medicine Case Reports
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Acceso en línea:http://www.sciencedirect.com/science/article/pii/S2213007126000936
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