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A rare metastatic mesenteric malignant PEComa with TSC2 mutation treated with palliative surgical resection and nab-sirolimus: a case report

Abstract Background Malignant perivascular epithelioid cell tumors (PEComas) are exceedingly rare malignant mesenchymal neoplasms with characteristic morphological and immunohistochemical (IHC) patterns. However, some malignant PEComas are poorly differentiated with atypical histopathological featur...

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Xehetasun bibliografikoak
Egile Nagusiak: Luke Meredith, Timothy Chao, Avinoam Nevler, Atrayee Basu Mallick, Rajan K. Singla, Peter A. McCue, Wilbur B. Bowne, Wei Jiang
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: BMC 2023-04-01
Saila:Diagnostic Pathology
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Sarrera elektronikoa:https://doi.org/10.1186/s13000-023-01323-x
Etiketak: Etiketa erantsi
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