PO75 | Prophylaxis with RFXIII: a clinical case in a pediatric patient with congenital FXIII deficiency and delayed diagnosis
Background: Congenital factor XIII (FXIII) deficiency is a rare coagulation disorder characterized by muscular or mucocutaneous bleeding with life-threatening intracranial hemorrhages (ICHs), especially in cases with severe disease. The best treatment is the use of prophylactic plasma-derived or re...
Salvato in:
| Natura: | Artigo |
|---|---|
| Lingua: | Inglês |
| Pubblicazione: |
PAGEPress Publications
2025-10-01
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| Serie: | Bleeding, Thrombosis and Vascular Biology |
| Soggetti: | |
| Accesso online: | https://www.btvb.org/btvb/article/view/344 |
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